Department of Pediatrics, Loghman Hakim Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran.
Abstract: (2906 Views)
Among nevoid causes of hypopigmentations; incontinentia pigmenti achromians (Hypomelanosis of Ito) is a neurocutaneous syndromes characterized by distinctive macular, linear or irregular whorls or swirls of Hypopigmentations. Unrelated to incontinentia pigmenti, the loss of pigment begins spontaneously during infancy or early childhood and is of Particular importance because of the falt that many patients have associated Internal anomalies and manifestations, (seizure disorders, delayed development, musculoskeletal anomalies or occular disturbances). A case of Hypomelanosis of Ito with generalized seizure was presented in a 7 month-old male; this will definitively discloses anthre rare cause of convulsion to look fore in pediatric practice.