Shaheed Beheshti University of Medical Sciences & Health Services,Iran.
Abstract: (1476 Views)
SUMMARY
X. Pis a rare autosomal recessive genodermatosis characteriseJ by photophohia, severe solar sensitivity, cutaneous pigmentary changes, xerosis and early Jevdopment of mucocutaneous and ocular
cancer particularly in sun exposeJ skin. Tumors whichinclude solar keratosis, cutaneous horn, keratoachanthoma, squamous and basal cell carcinoma, malignant melanoma and angioma may developeJ in late childhood. We have presented in this article a case of atypical fihroxanthoma in 12 year old girl with X.P.